Trilogy of Fallot
The trilogy of Fallot is a congenital heart disease consisting of the following defects: pulmonary valve stenosis, right ventricular hypertrophy and atrial septal defect. This disease is 1.6-1.8% of all congenital heart defects.
Trilogy of Fallot | |
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Specialty | Medical genetics |
Mechanism
It consists of the following:
The first two of these are also found in the tetralogy of Fallot. However, the tetralogy has a ventricular septal defect instead of an atrial one, and it also involves an overriding aorta.
Diagnosis
Clinically trilogy of Fallot can have cardiomegaly, less symptomatic when compared to ToF, JVP increased, a wave is more elevated, delayed P2, apex beat will be of LV type. S4+, ejection click+, On doing Cath, RV angiogram, when RV is flicked, to create a RV ectopic, there is post ectopic potentiation of the murmur, unlike ToF
Treatment
Thoracotomy is used to surgically correct this pathology.[1]
History
It is named in honor of its discoverer: Etienne Fallot.[2]
References
- Wang YQ, Chen RK, Ye WW, et al. (1999). "Open-heart surgery in 48 patients via a small right anterolateral thoracotomy". Tex Heart Inst J. 26 (2): 124–8. PMC 325616. PMID 10397435.
- synd/2283 at Who Named It?