Hereditary progressive mucinous histiocytosis

Hereditary progressive mucinous histiocytosis is a very rare, benign, non-Langerhans' cell histiocytosis. An autosomal dominant or X-linked hereditary disease described on the skin, it has been found almost exclusively in women.[1][2] One case of the disease in a male patient has been reported.[3]

Hereditary progressive mucinous histiocytosis
This condition is inherited in an autosomal dominant manner
SpecialtyDermatology

See also

References
  1. James, William D.; Berger, Timothy G.; et al. (2006). Andrews' Diseases of the Skin: clinical Dermatology. Saunders Elsevier. p. 718. ISBN 978-0-7216-2921-6.
  2. Antoni-Bach, N; Pfister, R; Grosshans, E; Kleinclaus, I; Boehm, N; Grange, F; Guillaume, J (2000). "Hereditary progressive mucinous histiocytosis". Annales de Dermatologie et de Vénéréologie. 127 (4): 400–4. PMID 10844262.
  3. Schlegel, C; Metzler, G; Burgdorf, W; Schaller, M (2010). "Hereditary progressive mucinous histiocytosis: First report in a male patient". Acta Dermato Venereologica. 90 (1): 65–7. doi:10.2340/00015555-0763. PMID 20107728.



Classification
External resources


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