Hemihydranencephaly
Hemihydranencephaly is a severe cephalic disorder characterized by complete or almost complete absence of the cerebral cortex with preservation of meninges, basal ganglia, pons, medulla, cerebellum, and falx. It is a special type of hydranencephaly.
Hemihydranencephaly | |
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Specialty | Neurology |
It is a very rare disease. As it stands, only 7 cases have been reported.
References
- Greco F, Finocchiaro M, Pavone P, Trifiletti RR, Parano E. Hemihydranencephaly: case report and literature review. J Child Neurol. 2001;16 :218–221
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