Chapel Hill Consensus Conference

The Chapel Hill Consensus Conferences (CHCC) (1994 and 2012) are a pair of international conferences which addressed the need of standardized classification system for systemic vasculitides.[1][2]

2012 Revised International Chapel Hill Consensus Conference Nomenclature of Vasculitides

Classification GroupDiseases
Large-vessel vasculitis (LVV)Takayasu Arteritis (TAK); Giant-cell arteritis (GCA)
Medium-vessel vasculitis (MVV)Polyarteritis nodosa (PAN), Kawasaki disease (KD)
Small vessel vasculitis (SVV)ANCA-associated vasculitis (AAV); Immune complex SVV
Variable vessel vasculitis (VVV)Behcet's disease (BD); Cogan's syndrome (CS)
Single Organ Vasculitis (SOV)Cutaneous leukocytoclastic angiitis; cutaneous arteritis; primary central nervous system vasculitis; isolated aortitis; others
Vasculitis associated with systemic diseaseLupus vasculitis; Rheumatoid vasculitis; Sarcoid vasculitis; others
Vasculitis associated with probable etiologyHepatitis C virus-associated cryoglobulinemic vasculitis; Hepatitis B virus-associated vasculitis; Syphilis-associated aortitis; Drug-associated immune complex vasculitis; Cancer-associated vasculitis; others

References

  1. Jeannette JC; Nomenclature of systemic vasculitides. Proposal of an international consensus conference; Arthritis Rheum 2013
  2. Jeannette, JC; Overview of the 2012 Revised International Chapel Hill Consensus Conference Nomenclature of Vasculitides; Clinical and Experimental Nephrology, 2013
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